{"id":25,"date":"2025-01-10T08:35:25","date_gmt":"2025-01-10T11:35:25","guid":{"rendered":"https:\/\/saude.novartis.com.br\/mielofibrose\/?p=25"},"modified":"2025-01-10T12:14:10","modified_gmt":"2025-01-10T15:14:10","slug":"o-que-e-mielofibrose","status":"publish","type":"post","link":"https:\/\/saude.novartis.com.br\/mielofibrose\/o-que-e-mielofibrose\/","title":{"rendered":"O que e\u0301 mielofibrose?"},"content":{"rendered":"\n<p>A <strong>mielofibrose \u00e9 um tipo de c\u00e2ncer no sangue<\/strong>, mais comum em <strong>pessoas acima dos 50 anos<\/strong>, no qual a medula \u00f3ssea, o tecido macio e esponjoso dentro dos ossos, se torna um tecido grosso e enrijecido. Essa altera\u00e7\u00e3o na medula \u00f3ssea <strong>prejudica a produ\u00e7\u00e3o das c\u00e9lulas do sangue<\/strong>, causando uma s\u00e9rie de transtornos \u00e0 sa\u00fade.<sup>1,2<\/sup><\/p>\n\n\n\n<div style=\"border-radius: 15px; border-style: solid; border-color: #dddddd; background-color: #f7f7f7; padding: 10px;\"\t>\n\t<div class=\"row\" style=\"align-content: center; margin: 10px; padding: 10px 20px;\">\n\t\t<h3>Neoplasias mieloproliferativas<\/h3>\n        <p>A mielofibrose pertence a um grupo de doen\u00e7as chamado neoplasias mieloproliferativas, no qual as c\u00e9lulas do sangue (gl\u00f3bulos vermelhos, gl\u00f3bulos brancos ou plaquetas) n\u00e3o s\u00e3o produzidas de modo adequado. Existem 6 tipos de neoplasias mieloproliferativas cr\u00f4nicas:<sup>3<\/sup>\n        <ul style=\"margin-left: 20px;\">\n          <li>Mielofibrose;<\/li>\n          <li>Policitemia vera;<\/li> \n          <li>Trombocitemia essencial;<\/li>\n          <li>Leucemia mieloide cr\u00f4nica;<\/li> \n          <li>Leucemia neutrof\u00edlica cr\u00f4nica;<\/li>\n          <li>Leucemia eosinof\u00edlica cr\u00f4nica.<\/li> \n        <\/ul>\n    <\/div>\n<\/div>\n\n\n\n<p><\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-full\"><img loading=\"lazy\" decoding=\"async\" width=\"700\" height=\"237\" src=\"https:\/\/saude.novartis.com.br\/mielofibrose\/wp-content\/uploads\/sites\/34\/2024\/12\/1-1-qual-a-causa-da-mielofibrose.png\" alt=\"\" class=\"wp-image-11\" srcset=\"https:\/\/saude.novartis.com.br\/mielofibrose\/wp-content\/uploads\/sites\/34\/2024\/12\/1-1-qual-a-causa-da-mielofibrose.png 700w, https:\/\/saude.novartis.com.br\/mielofibrose\/wp-content\/uploads\/sites\/34\/2024\/12\/1-1-qual-a-causa-da-mielofibrose-300x102.png 300w\" sizes=\"(max-width: 700px) 100vw, 700px\" \/><\/figure><\/div>\n\n\n<h3 class=\"wp-block-heading\">Qual a causa da mielofibrose?<\/h3>\n\n\n\n<p>A medula \u00f3ssea saud\u00e1vel produz c\u00e9lulas imaturas formadoras de sangue chamadas <strong>c\u00e9lulas-tronco<\/strong>, que podem se desenvolver em gl\u00f3bulos vermelhos, gl\u00f3bulos brancos ou plaquetas. <strong>Na mielofibrose, uma altera\u00e7\u00e3o (muta\u00e7\u00e3o) no DNA de uma c\u00e9lula-tronco<\/strong> faz com que a c\u00e9lula se torne anormal ou uma c\u00e9lula cancerosa, que se multiplica e passa a muta\u00e7\u00e3o para novas c\u00e9lulas.<sup>2<\/sup><\/p>\n\n\n\n<p>Com o tempo, mais c\u00e9lulas cancerosas s\u00e3o produzidas, gerando uma inflama\u00e7\u00e3o e, consequentemente, a forma\u00e7\u00e3o do tecido cicatricial na medula \u00f3ssea. A cicatriza\u00e7\u00e3o e o excesso de c\u00e9lulas cancerosas podem impedir a produ\u00e7\u00e3o adequada de c\u00e9lulas sangu\u00edneas saud\u00e1veis pela medula \u00f3ssea, comprometendo o transporte de oxig\u00eanio e nutrientes pelo corpo.<sup>2,4<\/sup><\/p>\n\n\n\n<div style=\"border-radius: 15px; border-style: solid; border-color: #dddddd; background-color: #f7f7f7; padding: 10px;\"\t>\n\t<div class=\"row\" style=\"align-content: center; margin: 10px; padding: 10px 20px;\">\n\t\t<h3>A mielofibrose est\u00e1 associada a muta\u00e7\u00f5es gen\u00e9ticas adquiridas, ou seja, altera\u00e7\u00f5es no DNA que n\u00e3o s\u00e3o herdadas.<sup>4<\/sup><\/h3>\n        <p>A muta\u00e7\u00e3o gen\u00e9tica mais comum em pacientes com mielofibrose \u00e9 no gene que produz a enzima Janus kinase tipo 2 (JAK2). Ela acontece entre 50% e 60% dos casos da doen\u00e7a. No entanto, tamb\u00e9m podem ocorrer muta\u00e7\u00f5es nos genes respons\u00e1veis pela produ\u00e7\u00e3o das prote\u00ednas CALR (25% dos pacientes) e MPL (5 a 10% dos pacientes).<sup>1,5,6<\/sup> <\/p>\n    <\/div>\n<\/div>\n\n\n\n<h3 class=\"wp-block-heading\">Classifica\u00e7\u00e3o da mielofibrose<\/h3>\n\n\n\n<p>Atualmente, os especialistas utilizam duas classifica\u00e7\u00f5es para a mielofibrose:<\/p>\n\n\n\n<p><b style=\"font-size: 1.2em; font-weight:bold; \">Mielofibrose prim\u00e1ria<\/b><br>\u00c9 a mielofibrose que se apresenta sem causa conhecida e com nenhuma liga\u00e7\u00e3o com outra doen\u00e7a.<sup>1<\/sup><\/p>\n\n\n\n<p><b style=\"font-size: 1.2em; font-weight:bold; \">Mielofibrose secund\u00e1ria<\/b><br>\u00c9 a mielofibrose decorrente de alguma outra doen\u00e7a j\u00e1 existente na medula \u00f3ssea, como por exemplo, a trombocitemia essencial (TE) ou a policitemia vera (PV), ambas pertencentes ao grupo das neoplasias mieloproliferativas.<sup>1<\/sup><\/p>\n\n\n\n<p>Em ambos os casos, o paciente corre o risco de evoluir para uma leucemia mieloide aguda (LMA), tipo de c\u00e2ncer que tem como principal caracter\u00edstica a superprodu\u00e7\u00e3o de c\u00e9lulas imaturas (que acabaram de nascer), tamb\u00e9m conhecidas por mieloblastos. Os mieloblastos, quando em grande quantidade na medula \u00f3ssea, bloqueiam a forma\u00e7\u00e3o dos demais componentes do sangue.<sup>1<\/sup><\/p>\n\n\n\n<!-- BARRA PROCURE ESPECIALISTA -->    \n<div style=\"border-radius: 15px; background-color: #f7f7f7; padding: 20px;\"\t>\n\t<div class=\"row\" style=\"align-content: center; margin: 20px;\"><center>\n\t<h2 style=\"color: #0066cc !important;\">Encontre um m\u00e9dico especialista em Mielofibrose!<\/h2>\n\t<\/center><\/div>\n\n\t<div class=\"wp-block-button\" style=\"color: #ff6600!important; margin-bottom: 10px;\"><center>\n\t\t<a class=\"wp-block-button__link has-white-color has-vivid-cyan-blue-background-color has-text-color has-background has-text-align-center wp-element-button\" style=\"background-color: #ff6600!important; color:#ffffff!important; text-decoration:none;\" href=\"https:\/\/novartismf.boaconsulta.com\/\" target=\"_blank\" rel=\"noopener\"><b>Busque especialista<\/b><\/a>\n\t<\/center><\/div>\n<\/div>\n<!-- BARRA PROCURE ESPECIALISTA -->\n\n\n\n<hr class=\"wp-block-separator has-alpha-channel-opacity\"\/>\n\n\n\n<p><small><strong>Refer\u00eancias:<\/strong><br><strong>1.<\/strong> Mielofibrose. ABRALE. Dispon\u00edvel em: https:\/\/abrale.org.br\/doencas\/mielofibrose\/o-que-e\/. Acesso em 08 de agosto de 2024.<br><strong>2.<\/strong> Myelofibrosis. Cleveland Clinic. Dispon\u00edvel em: https:\/\/my.clevelandclinic.org\/health\/diseases\/15672-myelofibrosis. Acesso em 08 de agosto de 2024.<br><strong>3.<\/strong> Chronic Myeloproliferative Neoplasms Treatment. NCI. Dispon\u00edvel em: https:\/\/www.cancer.gov\/types\/myeloproliferative\/patient\/chronic-treatment-pdq. Acesso em 08 de agosto de 2024.<br><strong>4.<\/strong> Myelofibrosis. Mayo Clinic. Dispon\u00edvel em: http:\/\/www.mayoclinic.org\/diseases-conditions\/myelofibrosis\/home\/ovc-20261141. Acesso em 08 de agosto de 2024.<br><strong>5.<\/strong> Myelofibrosis (MF). MPN Research Foundation. Dispon\u00edvel em: https:\/\/mpnresearchfoundation.org\/primary-myelofibrosis-pmf\/?gclid=EAIaIQobCh. Acesso em 08 de agosto de 2024.<br><strong>6.<\/strong> Myelofibrosis. Leukemia &amp; Lymphoma Society. Dispon\u00edvel em: https:\/\/www.lls.org\/myeloproliferative-neoplasms\/myelofibrosis. Acesso em 08 de agosto de 2024.<\/small><\/p>\n\n\n\n<hr class=\"wp-block-separator has-alpha-channel-opacity\"\/>\n\n\n\n<p><small>Material destinado ao p\u00fablico leigo. 2024 \u00a9 Direitos Reservados Novartis Bioci\u00eancias S\/A \u2013 Proibida a reprodu\u00e7\u00e3o total ou parcial n\u00e3o autorizada. Produzido em outubro\/2024.<\/small><\/p>\n\n\n\n<hr class=\"wp-block-separator has-alpha-channel-opacity\"\/>\n\n\n\n<p>BR-32368<\/p>\n","protected":false},"excerpt":{"rendered":"<p>A mielofibrose \u00e9 um tipo de c\u00e2ncer no sangue, mais comum em pessoas acima dos&#8230;<\/p>\n","protected":false},"author":2,"featured_media":10,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"footnotes":""},"categories":[10],"tags":[],"class_list":["post-25","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-mielofibrose"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v25.1 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>O que e\u0301 mielofibrose? - Mielofibrose<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/saude.novartis.com.br\/mielofibrose\/o-que-e-mielofibrose\/\" \/>\n<meta property=\"og:locale\" content=\"pt_BR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"O que e\u0301 mielofibrose? 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